EURORAD ESR

Case 15574

Late diagnosis of labyrinthine (Michel) aplasia in a 16-year-old girl with congenital anacusis

Author(s)
Kadish Lucien K, Tiona Micheline, Amriss Omar, Moussali Nadia, El Benna Naima

CHU IBN Rochd;
Casablanca, Morocco;
Email:kadishkayij@gmail.com
 
Patient
female, 16 year(s)
 
 
  • Figure 1
    Normal anatomy of the inner ear on CT
     

    Axial section image. Blue: Vestibule recess; Red: Lateral semi-circular canal; Green: Vestibular aqueduct; Orange: Posterior semi-circular canal.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Axial section image. Blue: Modiolus; Brown: Cochlea apical turn; Black: Cochlea middle turn; Purple: Vestibule recess; Light Blue: Posterior osseous ampulla; Orange: Posterior semi-circular canal.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Axial section image. Black: Cochlea middle turn; Brown: Cochlea basilar turn; Yellow: round window.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Coronal section image. Blue: Facial nerve canal tympanic segment; Green: Facial nerve canal labyrinthine segment; Red: Cochlea; Purple: Hamulus.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Coronal section image. Blue: Superior semi-circular canal; Red: Lateral semi-circular canal; Green: Vestibule recess; Orange: Internal acoustic canal.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;
     
     
  • Figure 2
    Labyrinthine aplasia: Left temporal bone CT
     

    Axial section image. IAC: Internal acoustic canal; Blue: Malleus head; Green: Incus body. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Axial section image. Blue: Malleus neck; Green: Incus long process. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Coronal section image also shows the absence of labyrinthine structures.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;
     
     
  • Figure 3
    Labyrinthine aplasia: Right temporal bone CT
     

    Axial section image. IAC: Internal acoustic canal; Blue: Malleus head; Green: Incus body; Orange: Facial nerve. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Axial section image. Blue: Malleus neck; Green: Incus long process. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;

    Coronal section image also shows the absence of labyrinthine structures.

     
    Area of Interest: Ear / Nose / Throat; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Congenital;
     
     
Axial section image. Blue: Vestibule recess; Red: Lateral semi-circular canal; Green: Vestibular aqueduct; Orange: Posterior semi-circular canal.
 
Axial section image. Blue: Modiolus; Brown: Cochlea apical turn; Black: Cochlea middle turn; Purple: Vestibule recess; Light Blue: Posterior osseous ampulla; Orange: Posterior semi-circular canal.
 
Axial section image. Black: Cochlea middle turn; Brown: Cochlea basilar turn; Yellow: round window.
 
Coronal section image. Blue: Facial nerve canal tympanic segment; Green: Facial nerve canal labyrinthine segment; Red: Cochlea; Purple: Hamulus.
 
Coronal section image. Blue: Superior semi-circular canal; Red: Lateral semi-circular canal; Green: Vestibule recess; Orange: Internal acoustic canal.
 
Axial section image. IAC: Internal acoustic canal; Blue: Malleus head; Green: Incus body. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.
 
Axial section image. Blue: Malleus neck; Green: Incus long process. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.
 
Coronal section image also shows the absence of labyrinthine structures.
 
Axial section image. IAC: Internal acoustic canal; Blue: Malleus head; Green: Incus body; Orange: Facial nerve. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.
 
Axial section image. Blue: Malleus neck; Green: Incus long process. There is absence of vestibule, cochlea, semicircular canals and vestibular aqueduct.
 
Coronal section image also shows the absence of labyrinthine structures.
 
 
 
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