Case 1798
J-shaped sella
Clinical History
Imaging Findings
Skull x-rays were performed to look for a vault fracture. The lateral skull x-ray is shown (Fig. 1). The sella turcica appears to be quite shallow because it is grossly elongated and has a shallow anterior convexity. The patient went on to have a CT scan of the brain, which showed no space-occupying lesions, leading to the conclusion that the sella in this patient was a normal variant.
Discussion
This may be rarely seen in normal adult skulls, but is a slightly more common appearance in the paediatric age group (incidence of 5-6%). Although it can arise as a normal variant certain underlying causes which can expand the sella need to be kept in mind when reviewing such films. The important pathological causes of such an appearance are chronic hydrocephalus and raised intracranial pressure, causes of 'gargoylism' such as Morquio's syndrome, Hunter's syndrome and other mucopolysaccharidoses, glioma of the optic chiasm and the 'empty sella syndrome'.
Final Diagnosis
MeSH
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Empty Sella Syndrome
[C19.700.320]
A condition associated with underdevelopment or absence of the diaphragma sellae which allows herniation of the meninges into the SELLA TURCICA. The pituitary gland becomes compressed against the walls of the sella and the sella may enlarge. Female gender; OBESITY; PSEUDOTUMOR CEREBRI; and pituitary ADENOMA are associated with this condition, which may present with HEADACHE. (From Joynt, Clinical Neurology, 1992, Ch36, p85)
References
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[1]Sutton D. The Skull. In Sutton D (ed) Textbook of Radiology and Imaging. Churchill Livingstone, London, p 1465 (1998).