CASE 751 Published on 01.01.2001

Cerebral band heterotopia

Section

Neuroradiology

Case Type

Clinical Cases

Authors

R.N.Sener

Patient

4 years, female

Categories
No Area of Interest ; Imaging Technique MR
Clinical History
Psychomotor retardation, and seizures.
Imaging Findings
Presented with moderate mental and motor retardation. Seizures were noted. An MR imaging examination was undertaken on a 0.5 Tesla unit. T1 and T2-weighted images were acquired.
Discussion
Band heterotopia is a rare type of neuronal migration disorders. A ribbon of heterotopic neurons is located circumferentially beneath the cerebral cortex. Incomplete types of band heterotopia can also occur. On imaging, the overlying cortex may appear normal, atrophic or it may show dysplastic areas. In diffuse band heterotopia such as in the current case, the atrophy-like pattern of the overlying cortex, could have resulted from a diffuse underdevelopment interfering with the abnormal process leading to band heterotopia. Therefore the term ‘hypoplasia’ may be more descriptive for cortical changes. Patients with band heterotopia may have serious symptoms such as psychomotor retardation, and seizures. Patients with relatively mild clinical presentations with normal social adaptation have also been reported. Such variations seem to be related to the condition of the overlying cortex.
Differential Diagnosis List
Band heterotopia
Final Diagnosis
Band heterotopia
Case information
URL: https://eurorad.org/case/751
DOI: 10.1594/EURORAD/CASE.751
ISSN: 1563-4086